Ewing sarcoma: symptoms, prognosis, treatment
Sarcoma Jung - a very aggressive tumorThe disease, which got its name after James Ewing, first described it. Most often, the disease develops in boys or boys from 5 to 30 years. At another age, the disease almost never occurs. Usually sarcoma is found in boys aged 10 to 15 years. Girls can also suffer from such a disease, but much less often. The disease occurs only in the white race.
Sarcoma is a variety of tumors,developing within the bone tissue. Most likely Ewing's sarcoma is localized in the pelvic bones, shoulder joints, tibia. However, it is often accompanied by multiple neuroectodermal neoplasms in soft tissues, peripheral neuroepitheliomas (retinal tumors), as well as Askin's tumor, which is most often localized in the thorax.
If a teenager has a weakness, an increasetemperature, swelling in the pelvic bones, shoulder girdle or tibia, an expert may suggest that this is the first stage of the disease, which is called Ewing's sarcoma. Symptoms develop very quickly.
Malaise, fever,progression of pain in the limb, over which the tumor develops. Neoplasm becomes hot to the touch, rapidly increases in size. Gradually on the site of the tumor, the vessels grow considerably, and the muscles become very tense. After a short time, the limb can not function fully. To make the correct diagnosis, doctors can stop the development of the disease only.
For diagnosis, use x-ray,ultrasound, bone scanning, take a tissue sample for a biopsy. The timely establishment of a diagnosis also helps to establish the degree of the disease.
In the localized stage, tumor formations are located in one part of the body. On a metastatic stage, neoplasms spread to the lungs, bones, bone marrow.
Is it possible to cure such a terrible disease as Ewing's sarcoma? The prognosis of the development of the disease often depends on the time of contact with specialists.
Usually early treatment allows you to get rid of the disease only with the help of procedures and medications, without resorting to limb amputation, rib removal or other surgery.
Unfortunately, the majority of patients with a diagnosisEwing's sarcoma is addressed to the doctor only when their state of health is extremely poor, and neoplasms have already metastasized. In this case, the surgical removal of the neoplasm, sometimes parts of the bone, is most often performed. In severe cases, limb amputation or rib removal is necessary.
Regardless of whether the operation is performed, all patients are prescribed chemotherapy, radiotherapy.
In any case, Ewing's sarcoma is treated no less, and sometimes more than a year.
And early treatment in 80% of cases leads to complete cure. If treatment is started when there were multiple metastases, the prognosis is much worse.
However, today there is a new radical methodtreatment of patients with poor prognosis. Complex radio, chemo-, radiotherapy is combined with bone marrow transplantation or stem cells, which significantly improves the indications.
What provokes the appearance of the disease? An exact answer to this question does not exist yet, but it is established that in 45% of cases of Ewing's sarcoma develops against the background of the received trauma. In addition, some abnormalities in the development of the skeleton and genitourinary system can affect its development.
Prevention of the disease does not exist, becausethe way of life does not affect the appearance of the disease. However, sensitive, attentive attitude to yourself, your health, timely access to a doctor greatly simplifies the diagnosis, allows you to achieve a cure. </ strong </ p>
